1 2 3 4 5 WT1 2 2 6 7 8 NPHS1 5 NPHS1 9 11 LMX1B 12 14 NPHS2 15 ACTN4 16 CD2AP 17 18 TRPC6 19 20 Podxl 21 NPHS1 Nphs1 22 23 NPHS1 Nphs1 23 22 24 LMX1B 12 14 Lmx1b 25 Lmx1b 26 27 28 Nphs2 Lmx1b Lmx1b 26 27 COL4A4 28 NPHS2 26 27 COL4A4 NPHS2 LMX1B NPHS2 27 NPHS2 26 NPHS2 27 29 Lmx1b 30 NPHS2 COL4A3 COL4A4 Lmx1b 30 1 Lmx1b 30 LMX1B Fig. 1 a–f Lmx1b Lmx1b arrows b Lmx1b d f +/lox Lmx1b lox/lox Lmx1b Cre NPHS2 Bars a b c f 30